journal article·2025-08-01Open access

Identification and clinical validation of immune-related genes as potential diagnostic and therapeutic targets in Kawasaki disease

Jin Ma, Yunjia Tang, Haitao Lv, Xiudao Song, Zhiheng Liu

AIP Advances· Volume 15· Issue 8

Abstract

Kawasaki disease (KD) is a systemic vasculitis with an unknown etiology, involving immune-related pathways and genes. This study aimed to identify immune-related differentially expressed genes (IR-DEGs) during the acute phase of KD and explore potential diagnostic and therapeutic targets. Three datasets were applied in this work, including GSE18606, GSE68004, and GSE63881. IR-DEGs were obtained from GSE18606 and ImmPort database. GO and KEGG analyses were performed on IR-DEGs. The expression levels of hub genes with an area under the curve (AUC) greater than 0.9 were evaluated using the external datasets and were investigated with the acute phase of KD. Molecular docking was employed to investigate the potential of these hub genes as drug targets. Four hub genes (CAMP, MMP9, S100A9, and S100A12) associated with immune were identified, which were confirmed by datasets GSE68004, GSE63881, and clinical experimental data. In the infiltration abundance of KD, B cells memory, T cells CD4 naïve, T cells CD4 memory activated, monocytes, mast cells activated, and neutrophils in the two groups were significantly different. Immune cell infiltration analysis further revealed that neutrophil was positively correlated with these four hub genes. Methotrexate and curcumin exhibit strong affinity for S100A12 and MMP9, indicating that these two drugs may modulate the inflammatory response in KD via S100A12 or MMP9. This study provides valuable biomarkers and treatment insights into KD, offering new perspectives for clinical management and prognosis.
Source: crossref · Quality: baseline

Research context

OpenAlex topics: Kawasaki Disease and Coronary Complications · Coronary Artery Anomalies · Inflammasome and immune disorders

SciVX discovery tags are terminology-based. OpenAlex topics are source-provided classifications.

Affiliations

Department of Pharmacy, Children’s Hospital of Soochow University 1 , Suzhou,

State Key Laboratory of Technologies for Chinese Medicine Pharmaceutical Process Control and Intelligent Manufacture, Nanjing University of Chinese Medicine 2 , Nanjing,

Department of Cardiology, Children’s Hospital of Soochow University 3 , Suzhou,

Traditional Chinese Medicine Science and Technology Transformation Center, Suzhou TCM Hospital Affiliated to Nanjing University of Chinese Medicine 4 , Suzhou,

Funding

National Natural Science Foundation of China · Science and Technology Program of Suzhou · Suzhou Gusu Health Talents Program

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